アブストラクト
Japanese
| Title | 当科における小児膵Solid pseudopapillary neoplasmに対する手術成績の検討 |
|---|---|
| Subtitle | 原著 |
| Authors | 福澤太一, 和田基, 佐々木英之, 工藤博典, 中村恵美, 安藤亮, 山木聡史, 大久保龍二, 仁尾正記 |
| Authors (kana) | |
| Organization | 東北大学病院小児外科 |
| Journal | 日本小児血液・がん学会雑誌 |
| Volume | 57 |
| Number | 3 |
| Page | 271-274 |
| Year/Month | 2020 / |
| Article | 原著 |
| Publisher | 日本小児血液・がん学会 |
| Abstract | 「要旨」【目的】膵solid pseudopapillary neoplasm(SPN)は若年女性に多くみられる比較的稀な低悪性度腫瘍で, 外科的切除により良好な予後が得られる疾患である. 今回, 当科におけるSPNの手術成績について検討した. 【対象と方法】1990年4月から2019年10月までに当科で外科的治療を施行したSPNを対象とし, 患者背景, 腫瘍発生部位, 治療経過, 転帰について診療録をもとに後方視的に検討した. 【結果】症例は6例で全例女児, 年齢は6歳 - 14歳(中央値10.5歳), 発生部位は膵尾部4例, 膵体部2例だった. 手術術式は, 脾合併膵体尾部切除術4例, 腫瘍核出術2例が施行された. 術後合併症は, 術中出血により術後輸血を必要とした貧血1例, 保存的に治療したgrade Bの術後膵液瘻(postoperative pancreatic fistula, POPF)を2例に認めた. 術後在院日数は8日 - 28日(中央値14.5日), 観察期間は1か月 - 122か月(中央値50.0か月)で全例無再発生存中である. 【考察】これまでの報告と同様, 女児に多くみられ予後は良好であった. 腫瘍が脾門部に進展している場合は脾動静脈との癒着が高度で剥離が困難なため全例で脾合併切除を施行したが, 腹腔鏡下に脾臓周囲の剥離を行うことは有用だった. 【結語】当科では膵SPNを6例経験し経過は良好だった. |
| Practice | 臨床医学：一般 |
| Keywords | 小児, 膵腫瘍, solid pseudopapillary neoplasm, children, pancreatic tumor |
English
| Title | Surgical outcomes for solid pseudopapillary neoplasm of the pancreas in children |
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| Subtitle | |
| Authors | Taichi Fukuzawa, Motoshi Wada, Hideyuki Sasaki, Hironori Kudo, Megumi Nakamura, Ryo Ando, Satoshi Yamaki, Ryuji Okubo, Masaki Nio |
| Authors (kana) | |
| Organization | Department of Pediatric Surgery, Tohoku University Hospital |
| Journal | The Japanese Journal of Pediatric Hematology/Oncology |
| Volume | 57 |
| Number | 3 |
| Page | 271-274 |
| Year/Month | 2020 / |
| Article | Original article |
| Publisher | The Japanese Society of Pediatric Hematology/Oncology |
| Abstract | [Abstract] Solid pseudopapillary neoplasm (SPN) of the pancreas is a low-grade malignancy that is rare in children. It often occurs in young women, and patients undergoing complete surgical resection show a favorable prognosis. In this study, we investigated treatment outcomes of SPN in our department. We retrospectively reviewed the medical records of six patients with SPN treated in our department between 1990 and 2019. Demographic characteristics, tumor localization, rendered treatment, and outcomes were assessed. All six patients were girls. Their ages at the time of surgery were 6 - 14 years (median 10.5 years). The tumor localization was the pancreatic body in two patients and the tail in four patients. Four patients underwent distal pancreatectomy with splenectomy and two patients underwent enucleation. Postoperatively, one patient required transfusion because of intraoperative bleeding, and two patients developed grade B postoperative pancreatic fistula (POPF). The postoperative course was uneventful in the other patients. Postoperative hospital stay was 8 - 28 days (median 14.5 days), and the follow-up period was 1 - 122 months (median 50.0 months). All six patients were alive without recurrence. Surgical outcomes of SPN were favorable in our case series. Although splenic preservation was difficult in patients with SPN affecting the splenic hilum, laparoscopic mobilization of the spleen was useful during tumor resection in these patients. |
| Practice | Clinical medicine |
| Keywords | children, pancreatic tumor, solid pseudopapillary neoplasm |
- 全文ダウンロード： 従量制、基本料金制の方共に770円(税込) です。
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残りの13件を表示する
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